A Case of Adrenocorticotropin -Independent Macronodular Adrenal Hyperplasia (AIMAH)- A Case Report
نویسندگان
چکیده مقاله:
The case-report is about a 47 year old woman with adrenocorticotropin-independent macronudular adrenal hyperplasia (AIMAH), with is a rare cause of endogenous Cushing’s syndrome. Urin free cortisol (UFC) and cortisol of 8AM were elevated along with the suppressed level of ACTH. Abdominal CT scan showed macronodules in both adrenals .The patient underwent left adrenalectomy and pathological data confirmed the diagnosis. The patient has been inhormon replacement therapy after surgery.
منابع مشابه
Adrenocorticotropin-Independnt Bilateral Adrenal Macronodular Hyperplasia (AIMAH) A Case Report
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Adrenocorticotropic hormone- (ACTH-)independent macronodular adrenal hyperplasia (AIMAH) is an infrequent cause of Cushing's syndrome (CS). AIMAH presents as incidental radiological finding or with subclinical or overt CS, occasionally with secretion of mineralocorticoids or sex steroids. The pathophysiology of this entity is heterogeneous. The aberrant adrenal expression and function of one or...
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1 of 2 DESCRIPTION Figure 1 is of a CT scan showing bilateral macronodular adrenal glands in a patient with adrenocorticotropic hormone-independent macronodular adrenal hyperplasia (AIMAH). AIMAH was fi rst described in 1964 1 . AIMAH is often discovered as a fortuitous radiological fi nding, as in our patient, or during investigation for endogenous hypercortisolism. AIMAH represents less than ...
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عنوان ژورنال
دوره 11 شماره 1
صفحات 76- 78
تاریخ انتشار 2019-03
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